Congenital complete absence of pericardium in a young woman with non-specific symptoms.

Congenital complete absence of pericardium in a young woman with non-specific symptoms

CONGENITAL PARTIAL PERICARDIAL DEFECT WITH HERNIATION OF THE LEFT ATRIAL APPENDAGE

Congenital defects of the pericardium are considered rare. Until 1979 , the reported cases were only about 200.1 Total absence of the left pericardium is the most common defect2 and less common is a partial defect of the left pericardium. Other types, i.e. isolated right-sided defects, total pericardial absence and diaphragmatic pericardial defects are very rare.3 Before the last decade, t...

Congenital complete absence of the pericardium.

A38-year-old woman with ill-defined chest pain had an abnormal x-ray 8 years before her only pregnancy. She had been unable to bear down during delivery, but gestation was otherwise uncomplicated, yielding a normal female offspring. She subsequently experienced left-sided chest pain that awakened her from sleep when turning into either a right or left lateral decubitus position. The pain was pu...

Congenital defects of the pericardium: a review.

Pericardial defects are a rare disorder that can be characterized as acquired or congenital. Congenital defects can be further characterized by location and size of the defect, e.g. left- or right-sided and partial or complete absence of the pericardium. While physical examination and electrocardiogram are not diagnostic, chest radiographs and echocardiography have findings that should alert th...

Bronchogenic cyst associated with congenital absence of the pericardium

We report a rare case of bronchogenic cyst associated with congenital complete absence of the pericardium. A 17-year-old male was admitted to the hospital for surgical resection of a growing cystic lesion located in the middle mediastinum. The patient was asymptomatic and no significant findings were found on physical examination. Resection of the mediastinal cyst was performed by video-assiste...